Journal des troubles sanguins et de la transfusion

Abstrait

Basal Ganglia Infarct in an Infant with Sickle Cell Disease - A Rare Association

Smita Mahapatra, Sitaram Mahapatra, Sudha Sethy, Rupa Das, Pranati Mohanty and Kalyani Hazra

Cerebrovascular accidents are common in elderly people, but rare in children. The stroke developing due to basal ganglion infarct in an infant with sickle cell disease (homozygous) is extremely rare. To the best of our knowledge, not a single case has been repoted till date. We are reporting a 10 months old infant developing stroke after a mild fall. The child was diagnosed of lacunar basal ganglion infarct in MRI. No abnormality was detected in routine hematological check-up and coagulation profile. But, sickling test was positive and confirmed of Sickle Cell Disease (SCD) in Hemoglobin electrophoresis (capillary zone). Although extremely rare, while dealing with stroke in infants and children, possibility of SCD should always be kept in mind.