Santé bucco-dentaire et gestion dentaire

Abstrait

Complex oral rehabilitation of a patient with Witkop?s syndrome: an interdisciplinary approach

Krisztina Mikul?s, P?ter Kivovics, G?bor Nagy, Krisztina M?rton, Melinda Madl?na

Witkop?s syndrome - a gentle form of ectodermal dysplasia - is a rare autosomal dominant disease manifested by defects of the nail plates of the fingers and toes, hypodontia or anodontia with normal hair and sweat gland function. Other ectodermal tissues, organs do not show any alteration. Oral manifestations may include incomplete development of both primary and permanent tooth germs. The location and form of erupted teeth could be irregular. This case report of a 23-year-old woman reveals the importance of a complex interdisciplinary dental treatment. Clinical examination ascertained lack of numerous permanent teeth: besides the numerous deciduous teeth, only maxillary first incisors, first molars and mandibular first molars were present in the mouth. Authors, an interdisciplinary team of surgeons, orthodontists, and prosthodontists proposed the complex rehabilitation of the patient with fixed prosthesis, and emphasize the importance of the long term follow up of the patient.