Journal de chirurgie et d'anesthésie

Abstrait

Review of Anesthetic Management of Myotonic Dystrophy and A Case Report of Sedation with Dexmedetomidine

Elena Garcia-Fernandez, Anna Grzanka, Pablo Redondo-Martinez, Maria Dolores Pato-Rodriguez, Ernesto Martinez-Garcia

15 year-old male patient, with Steinert’s Desease, was proposed for orthopedic surgery in left foot. He was sedated by continous perfusión of dexmedetomidine and an ultrasound-guided popliteal block was performed. The level of sedation achieved was adequate, without observing further adverse effects except of bradycardia with initial bolus. Dexmedetomidine was proved to be useful in this case; however, use of the drug should be carefully started at a low initial dose in patients with myotonic dystrophy. We also have reviewed the recent cases-report in patients with DM in past 15 years with a descriptive analysis.